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1、Descriptionsidiopathicgeneralizedepilepsy(简述特发性全面性癫痫)Idiopathicgeneralizedepilepsyandage-related.SincethecommencementoftheclinicalsymptomsandEEGchangesisbilateralsymmetry,nosignsofnervelocalization,EEGnormalbackgroundactivity.特发性全面性癫痫和年龄有关。临床症状和脑电图变化自开始即为双侧对称,无神经定位体征,脑电图背景活动亦正常。 (1)benignfamilialn
2、eonatalconvulsionsrare,autosomaldominant,mostborn2to3daysaftertheonsetofclonicepisodes.NospecialEEG.Historyandexaminationnoetiologyfoundthatapproximately14%ofthepatientslaterdevelopedintoatonic-clonicseizures,buttheprognosisisgood. (1)良性家族性新生儿惊厥较罕见,为常染色体显性遗传,大多数生后2~3天发病,表现为阵挛或窒息发作。无特殊脑电图表现。病史和检查无病
3、因发现,约14%的患者以后发展为强直--阵挛发作,但预后良好。 (2)benignneonatalconvulsionsrepeatedclonicortheepisodesmostcommon,andnoknowncauseandmetabolicdisordersappearedaboutfivedaysafterbirth.InterictalEEGoftenvariablesharpwaves,norecurrent.Psychomotordevelopmentalunaffected.locatedintheTomb,DongShenJiabang,deferthenextday
4、focusedontheassassination.Linping,Zhejiang,1ofwhichliquorwinemasters(WuzhensaidinformationisCarpenter),whogotAfewbayonets,duetomissedfatal,whennightcame (2)良性新生儿惊厥以出生后第5天左右出现反复阵挛或窒息发作最为常见,无已知病因和代谢障碍。发作间期脑电图常有可变的尖波,无反复发作。精神运动方面发育不受影响。 (3)benignmyoclonicepilepsyofinfancybornafter1to2yearsoldtransie
5、ntgeneralizedmyoclonicseizures,oftenconvulsionsorafamilyhistoryofepilepsy.TheearlysleepEEGrecordsshowbriefuniversalityspine-slowwave,pubertymayoccurtonic-clonicseizures,appropriatetreatmentiseasytocontrol.Mayhaveacertaindegreeofintelligenceretardationandmildpersonalitydisorder. (3)婴儿期良性肌阵挛癫痫出生后1~2
6、岁出现短暂性全身肌阵挛发作,常有惊厥或癫痫家族史。早期睡眠脑电图记录显示短暂普遍性棘—慢波,青春期可能发生强直—阵挛发作,适当治疗易于控制。可有一定程度智能发育迟滞和轻度人格障碍。 (4)childhoodabsenceepilepsy(frequentabsencepetitmal)isfoundinthe6to7-year-oldschool-agechildren,morecommoninwomen,significantgeneticpredisposition,autosomaldominantinheritancewithincompletepenetrancecharacte
7、rizedbyfrequentabsencessmallattackseveraltimesadaytodozensofadultmaybecured,orcontinuetohaveonlyabsenceseizuresortonic-clonicseizures.EEGshowed3Hzspike-slowwave,normalbackground,caninducehyperventilation.