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ID:5856801
大小:2.92 MB
页数:28页
时间:2017-12-14
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1、HYPERCORTISOLISMCUSHINGSYNDROMEContentsWhatisCushingsyndrome?Whatisthecauses?Howtodiagnose?ClinicalFeaturesHormonelevelsFunctionaltestLocalizationHowtotreatment?ContentsWhatisCushingsyndrome?Whatisthecauses?Howtodiagnose?ClinicalFeaturesHormonelevelsFunctionaltestLocalizationHowtotreatment?Definitio
2、nCushingSyndromeAdiversesymptomcomplexresultingfromexcesssteroidhormone(cortisol)productionCushingDiseaseAhypercortisolismresultingfrompituitaryACTHhypersecretionContentsWhatisCushingsyndrome?Whatisthecauses?Howtodiagnose?ClinicalFeaturesHormonelevelsFunctionaltestLocalizationHowtotreatment?CapsulaG
3、lomerulosaFasciculataReticularisMedullaAldosteroneAndrogenCatecholamineAdrenalStructureCortisolCortisolSecretionRegulationACTHCRHCortisolHypothalamusPituitaryAdrenalCausesofCushingSyndromeACTHCRHCortisolHypothalamusPituitaryAdrenalEctopicCRHsyndromeHypothalamusCushingsyn.Cushingdisease(CD)EctopicACT
4、HsyndromeAdrenaladenomaAdrenalcarcinomaMicronodularadrenaldiseaseMassivemacronodularadrenaldiseaseCausesofCushingsyndrome1.EndogenousCushingsyndrome(1)ACTH-dependentCushingdisease(CD)EctopicACTHsyndromeEctopicCRHsyndrome(2)ACTH-independentAdrenaladenomaAdrenalcarcinomaMicronodularadrenaldiseaseMassi
5、vemacronodularadrenaldisease(3)Pseudocushingsyndrome2.ExogenousCushingsyndromeContentsWhatisCushingsyndrome?Whatisthecauses?Howtodiagnose?ClinicalFeaturesHormonelevelsFunctionaltestLocalizationHowtotreatment?FunctionClinicalFeaturesFunctionsClinicalFeaturesFatCentralobesity,“moonface”“buffalohump”Pr
6、oteinThinextremities,muscleweakness,Purplestriae,bruising,osteoporosisGlucoseIGT,DMElectrolyteHypertension,hypokalemia,alkalosisFunctionsClinicalFeaturesImmunityInfection,impairedwoundhealingSexglandHirsutism,acne,menstrualdysfunction,ErectiledysfunctionBonemarrowIncreasedRBCandWBC,plethoricMentalIn
7、creasedlabilitySkinHyperpigmentationFunctionClinicalFeaturesHormoneLevel1.CortisollevelsPlasmacortisolrhythm(8Am,4Pm,midnight)24hUrinaryfreecortisol,17-OHCS,17-KSPlasmaACTHrhythm2.FunctionalTestsLowdo
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