Chiari畸形II型MRI病例图片影像诊断分析报告

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1、实用文档Chiari畸形II型(ChiariIIMalformation)MRI病例图片影像诊断分析【临床病史】：患者，2天的婴儿，胎儿期超声检查发现异常。2-day-oldinfantnotedtohaveanabnormalityonprenatalultrasound.【影像图片】MRI图像文案大全实用文档文案大全实用文档文案大全实用文档【影像表现】：T1-weightedsagittalimages(Figure1andFigure2)andT2-weightedaxialimages(Figure

2、3,Figure4,andFigure5)ofthebraindemonstrateasmallposteriorfossawithherniationofthecerebellartonsilsthroughtheforamenmagnum(bluearrows)andabeakedappearanceofthetectum(greenarrow).Thereisassociatedhydrocephalus(redarrow).文案大全实用文档文案大全实用文档T2-weightedsagittal(Fi

3、gure6andFigure7)andaxial(Figure8andFigure9)imagesofthespinedemonstrateamyelomeningoceleatthelevelofthelowerlumbarspine(purplearrows).文案大全实用文档文案大全实用文档【影像诊断】：ChiariIIMalformationChiari畸形II型【诊断要点】：ChiariIImalformationsarecomplexcongenitaldeformitiesinvolvingt

4、hebrainstemandcerebellumwithahostofassociateddevelopmentalabnormalitiesChiariII型畸形是一种复杂的先天畸形，累及脑干和小脑半球，常有许多伴随的发育异常。Thereisdisplacementofthebrainstemandlowercerebellumintothecervicalspinalcanalandamyelomeningoceleisalmostalwayspresent.脑干和小脑下部移位至颈椎管内并且常常会出现脊

5、膜膨出。【讨论】：TheChiariIImalformationisacomplexanomalywithskull,dural,brain,spinalandspinalcordmanifestations.Itisregardedasadiseaseofprimaryneurulationandisalmostinvariablyassociatedwithamyelomeningocele.Therearemultipleassociatedfindings,toinclude;protrusiono

6、fthecerebellartonsilsthroughtheforamenmagnum,extensionofthecerebellarhemispheresandvermisabovetheincisuraofthetentorium,beakedappearanceofthetectum,fenestrationofthefalx,hydrocephalus,aprominentmassaintermedia,colpocephaly,anddysgensisofthecorpuscallosum.C

7、hiariII型畸形是一种复杂的先天畸形，主要有颅骨、硬膜、颅脑、脊椎、脊髓异常表现。被认为是一种原始的神经胚形成病变，几乎都伴有脊膜膨出。同时还有多种伴发的异常，包括小脑扁桃体通过枕骨大孔下疝，小脑半球拉长呈塔状、小脑蚓部超过小脑幕切迹，被盖呈鸟嘴样改变，脑积水、中间块突出，空洞脑、胼胝体发育不良。TheChiariIImalformationisthemostcommonseriousmalformationoftheposteriorfossa,withafrequencyofapproximatel

8、y1caseper1000population.Hindbraindysfunctionisthemajorcauseofmortality.Themortalityrateis15%inthefirstfewyearsoflifeandisreportedtobeashighas50%forthelongtermrate,regardlessofthetreatmentstrategy.ChiariII型畸形是