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时间:2019-06-21
《胡桃夹综合征并发IgA肾病临床分析》由会员上传分享,免费在线阅读,更多相关内容在行业资料-天天文库。
1、万方数据胡桃夹综合征并发IgA肾病临床分析王耀敏张晓辉何强吴建永陈江华【摘要】目的了解胡桃夹综合征并发IsA肾病的l临床特点及提高其相应诊治水平。方法回顾分析14例胡桃夹综合征并发lSA肾病患者(病例组)及同期36例单纯胡桃夹综合征患者(对照组)的临床资料。所有胡桃夹综合征病例均由彩色多普勒超声和磁共振血管成像(MRA)诊断;lsa肾病均由病理证实。记录两组实验室、影像学资料并进行t检验分析。结果两组患者性别、年龄、血压差异无统计学意义。病例组Scr值高于对照组【(81.2±21.3)p.mol/L比(61.2±11.8
2、)I-Lmol/L,P<0.01】,尿蛋白量较多【(1.1±0.6)g/d比(0.3士0.2)g/d,P<0.011,血尿更明显(尿红细胞计分2.3±0.9比1.5±1.3,P<0.05)。彩色多普勒超声显示两组左肾静脉狭窄处及近肾门处血流速度和内径差异无统计学意义;磁共振血管成像提示两组患者肠系膜上动脉与腹主动脉之间的夹角差异无统计学意义。结论对持续存在血尿和蛋白尿、异常红细胞比例较高的胡桃夹综合征患者应考虑存在并发慢性肾炎特别是IsA肾病的可能,应及早行肾活检明确诊断。【关键词】肾小球肾炎,IrA;血尿;胡桃夹综合征
3、;彩色多普勒超声;磁共振血管成像ClinicalanalysisofnutcrackersyndromecomplicatedwithIgAnephropathyWANGYao—min,ZHANGXiao·hui,HEQmg,WUJian-yong,CHENJiang-hua.KidneyD厶emeCenter,theFirstAffiliatedHospital,CollegeofMedwine,刃aejiangUniversity,Hangzhou310003,ChinaCorrespondingauthor:CHE
4、NJiang-hua,Email:chenyianghua@zju.edtt.cn【Abstract】objectiveToelucidatetheclinicalfeaturesofnutcrackersyndromecomplicatedwitllIgAnephropathy(IsAN)andtoincreaseitslevelofdiagnosisandtreatment.MethodsClinicaldataof14casesofnutcrackersyndromecomplicatedwithlgAnephro
5、pathy(patientgroup)and36ca目gsofnutcrackersyndrome(controlgroup)Wereanalyzedretrospectively.Nutcrackersyndromewasdiagnosedbyultrasonographyandmagneticresonanceangiography(MRA)andIgANbyrenalbiopsy.DifferencesofclinicaldataandimagesintwogroupsWereanalyzed.ResultsGen
6、der,ageandbloodpressureoftwogroupswerenotsignificantlydifferent.HigherScrlevel【(81.2±21.3)p,mollLvs(61.2±11.8)Ixmol/L,P<0.Oil,moreseverepmteinufia【(1.1±0.6)g/dVS(O.3±O.2)g/d,P<0.01】andhematuria(2.3±0.9VS1.5±1.3,P<0.05)inpatientgroupwerefound.Differencesofultrason
7、ographyandMRAintwogroupswerenotsignificant.ConclusionRenalbiopsyshouldbeconsideredincasesofnutcrackersyndromewithpersistenceofprotcinuria,hematufiaorabnormalmorphologyofurinaryredbloodcell.【Keywords】Glomerolonephritis,IgA;Hematuria;Nutcrackersyndrome;Ultrasonogra
8、phy;MagneticresonanceangiographyIgA肾病是最常见的慢性肾小球肾炎,也是引起终末期肾病的重要病因之一,在亚洲地区占DOI:10.3760/cma.j.issn.1001—7097.2010.01.008作者单位:310003杭州,浙江大学医学院附属第一医院肾脏病中心通信作者:陈江华。E
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